Extraskeletal Myxoid Chondrosarcoma

Pronunciation

Definition 1

A rare malignant soft tissue neoplasm of uncertain lineage characterized by the presence of chondroblast-like cells in a myxoid stroma and a multinodular growth pattern. The most common sites of involvement are the deep soft tissues of the extremities, particularly the thigh. It usually presents as an enlarging soft tissue mass. Patients may have long survivals, but local recurrences and metastases occur in approximately half of the cases. The most common site of metastasis is the lungs. (NCI Thesaurus)

Definition 2

A malignant soft tissue tumor characterized by multinodular architecture, abundant myxoid matrix and malignant chondroblast-like cells arranged in cords, clusters or delicate networks. There are recurrent cytogenetic aberrations: t(9;22)(q22;q12) and t(9;17)(q22;q11). (NCI Thesaurus)

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Extraskeletal

Outside of or excluding the skeleton.